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Richard J H Smith Selected Research

Richard J H Smith Research Topics

Disease

46Hearing Loss (Hearing Impairment)
12/2023 - 05/2002
25Deafness (Deaf Mutism)
06/2023 - 05/2002
20Membranoproliferative Glomerulonephritis (Membranoproliferative Glomerulonephritis, Type II)
01/2024 - 09/2007
18Atypical Hemolytic Uremic Syndrome
11/2023 - 02/2009
17Glomerulonephritis
10/2022 - 05/2010
16Nonsyndromic Deafness
05/2020 - 05/2002
8Chronic Kidney Failure (Chronic Renal Failure)
01/2022 - 02/2011
8Otosclerosis
05/2012 - 09/2007
7Proteinuria
01/2024 - 09/2007
6Recurrent respiratory papillomatosis
03/2022 - 11/2002
5Paraproteinemias (Monoclonal Gammopathy)
01/2024 - 09/2013
5Inflammation (Inflammations)
10/2022 - 06/2008
5Rare Diseases (Rare Disease)
10/2022 - 09/2007
4Kidney Diseases (Kidney Disease)
01/2024 - 12/2017
4Renal Insufficiency (Renal Failure)
10/2022 - 05/2005
4Sensorineural Hearing Loss
01/2022 - 12/2010
3Disease Progression
02/2024 - 09/2005
3Pendred syndrome
01/2023 - 02/2002
3Monoclonal Gammopathy of Undetermined Significance
10/2022 - 11/2010
3Infections
01/2022 - 06/2016
3Thrombocytopenia (Thrombopenia)
11/2020 - 02/2011
3Autosomal Dominant 5 Deafness
05/2020 - 08/2005
3Thrombotic Microangiopathies
01/2020 - 01/2014
3Male Infertility (Male Sterility)
01/2018 - 04/2009
324 Autosomal Recessive Deafness
03/2010 - 05/2007
2Hemolysis
01/2023 - 01/2019
2Pierre Robin Syndrome (Syndrome, Pierre Robin)
01/2021 - 03/2020
2B-Cell Chronic Lymphocytic Leukemia (Chronic Lymphocytic Leukemia)
01/2018 - 09/2013
2Auditory neuropathy
08/2015 - 01/2008
2Inborn Genetic Diseases (Disease, Hereditary)
03/2014 - 08/2011
2Pathologic Constriction (Stenosis)
05/2011 - 04/2004
2Usher Syndromes (Usher Syndrome)
08/2010 - 06/2009
2Papilloma (Papillomatosis)
04/2010 - 11/2002
2Branchio-Oto-Renal Syndrome (Branchio Oculo Facial Syndrome)
04/2007 - 09/2004
2Carcinogenesis
01/2006 - 11/2005
1Persistent Infection
01/2024
1Myasthenia Gravis
01/2023
1Paroxysmal Hemoglobinuria (Paroxysmal Nocturnal Hemoglobinuria)
01/2023
1Neuromyelitis Optica (Devic's Disease)
01/2023
1Complement Factor I Deficiency
12/2022
1Atrophy
10/2022
1Fibrosis (Cirrhosis)
10/2022
1Asthma (Bronchial Asthma)
03/2022
1Respiratory Insufficiency (Respiratory Failure)
03/2022

Drug/Important Bio-Agent (IBA)

37Complement System Proteins (Complement)IBA
02/2024 - 10/2004
17Proteins (Proteins, Gene)FDA Link
01/2024 - 11/2002
14Dichlorodiphenyldichloroethane (DDD)IBA
01/2019 - 09/2007
13DNA (Deoxyribonucleic Acid)IBA
12/2018 - 08/2003
8Connexin 26IBA
08/2012 - 08/2002
6Antigen-Antibody Complex (Immune Complex)IBA
01/2024 - 05/2009
6Complement Factor H (Factor H)IBA
09/2021 - 05/2005
6Capsules (Microcapsules)IBA
05/2012 - 09/2007
5CreatinineIBA
01/2024 - 04/2016
5Complement Factor B (Factor B)IBA
11/2020 - 05/2010
4NucleotidesIBA
12/2016 - 11/2005
4Immunoglobulins (Immunoglobulin)IBA
06/2016 - 05/2009
3Biomarkers (Surrogate Marker)IBA
02/2024 - 06/2015
3Anti-Bacterial Agents (Antibiotics)IBA
01/2022 - 11/2003
3Complement C3 (C3 Complement)IBA
01/2021 - 04/2015
3MicroRNAs (MicroRNA)IBA
01/2019 - 03/2010
3Mitochondrial DNA (mtDNA)IBA
05/2015 - 01/2006
3ConnexinsIBA
07/2011 - 12/2003
3Nonsense Codon (Nonsense Mutation)IBA
02/2011 - 02/2007
3cyclonite (RDX)IBA
03/2010 - 05/2007
2ProteomeIBA
06/2023 - 02/2023
2eculizumabFDA Link
01/2023 - 09/2007
2Serine Proteases (Serine Protease)IBA
12/2022 - 01/2008
2chemotactic factor inactivatorIBA
12/2022 - 11/2012
2Complement Factor I (C3b Inactivator)IBA
12/2022 - 11/2012
2Complement Membrane Attack Complex (Membrane Attack Complex)IBA
10/2022 - 06/2015
2AminoglycosidesIBA
01/2022 - 06/2011
2Antineutrophil Cytoplasmic Antibodies (ANCA)IBA
05/2016 - 07/2012
2Rituximab (Mabthera)FDA Link
09/2013 - 09/2007
2Dexamethasone (Maxidex)FDA LinkGeneric
09/2013 - 12/2010
2Cidofovir (Vistide)FDA Link
04/2010 - 11/2005
2Ethylnitrosourea (N-Ethyl-N-nitrosourea)IBA
09/2009 - 08/2009
2Fibrinogen (Factor I)FDA Link
02/2009 - 02/2009
2Transforming Growth Factor beta (TGF-beta)IBA
04/2008 - 09/2007
2CytosineIBA
01/2007 - 11/2005
2Messenger RNA (mRNA)IBA
01/2007 - 11/2002
2Myosins (Myosin)IBA
11/2005 - 05/2002
1AutoantibodiesIBA
02/2024
1ReninIBA
11/2023
1Aquaporin 4IBA
01/2023
1Phenobarbital (Luminal)FDA Link
01/2023
1Complement C3 Nephritic FactorIBA
10/2022
1pembrolizumabIBA
03/2022
1Adrenal Cortex Hormones (Corticosteroids)IBA
03/2022
116S Ribosomal RNAIBA
01/2022
1Immunoglobulin G (IgG)IBA
09/2021
1Bevacizumab (Avastin)FDA Link
01/2021

Therapy/Procedure

16Therapeutics
12/2023 - 10/2002
8Cochlear Implantation
01/2022 - 02/2002
6Cochlear Implants (Cochlear Implant)
01/2022 - 05/2002
3Transplantation
01/2022 - 02/2009
2Otoscopes
11/2020 - 05/2020
2Lasers (Laser)
01/2017 - 05/2011
1Organ Transplantation
10/2022
1Complementary Therapies (Alternative Medicine)
01/2022
1Distraction Osteogenesis
01/2021